OTHER FORMS OF HEART DISEASE (420-429)

• 420 Acute pericarditis
  • Includes: acute:
    • mediastinopericarditis
    • myopericarditis
    • pericardial effusion
    • pleuropericarditis
    • pneumopericarditis
  • Excludes: acute rheumatic pericarditis (391.0)
    • postmyocardial infarction syndrome [Dressler's] (411.0)
  • 420.0 Acute pericarditis in diseases classified elsewhere
    • Code first underlying disease, as:
      • actinomycosis (039.8)
      • amebiasis (006.8)
      • nocardiosis (039.8)
      • tuberculosis (017.9)
      • uremia (585)
    • Excludes: pericarditis (acute) (in):
      • Coxsackie (virus) (074.21)
      • gonococcal (098.83)
      • histoplasmosis (115.0-115.9 with fifth-digit 3)
      • meningococcal infection (036.41)
      • syphilitic (093.81)
  • 420.9 Other and unspecified acute pericarditis
    • 420.90 Acute pericarditis, unspecified
      • Pericarditis (acute):
        • NOS
        • infective NOS
        • sicca
    • 420.91 Acute idiopathic pericarditis
      • Pericarditis, acute:
        • benign
        • nonspecific
        • viral
    • 420.99 Other
      • Pericarditis (acute):
        • pneumococcal
        • purulent
        • staphylococcal
        • streptococcal
        • suppurative
      • Pneumopyopericardium
      • Pyopericardium
      • Excludes: pericarditis in diseases classified elsewhere (420.0)
• 421 Acute and subacute endocarditis
  • 421.0 Acute and subacute bacterial endocarditis
    • Endocarditis (acute) (chronic) (subacute):
      • bacterial
      • infective NOS
      • lenta
      • malignant
      • purulent
      • septic
      • ulcerative
      • vegetative
    • Infective aneurysm
    • Subacute bacterial endocarditis [SBE]
    • Use additional code, if desired, to identify infectious organism [e.g., Streptococcus 041.0, Staphylococcus 041.1]
  • 421.1 Acute and subacute infectiveendocarditis in diseases classified elsewhere
    • Code first underlying disease, as:
      • blastomycosis (116.0)
      • Q fever (083.0)
      • typhoid (fever) (002.0)
    • Excludes: endocarditis (in):
      • Coxsackie (virus) (074.22)
      • gonococcal (098.84)
      • histoplasmosis (115.0-115.9 with fifth-digit 4)
      • meningococcal infection (036.42)
      • monilial (112.81)
  • 421.9 Acute endocarditis, unspecified
    • Endocarditis, acute or subacute
    • Myoendocarditis, acute or subacute
    • Periendocarditis, acute or subacute
    • Excludes: acute rheumatic endocarditis (391.1)
• 422 Acute myocarditis
  • Excludes: acute rheumatic myocarditis (391.2)
  • 422.0 Acute myocarditis in diseases classified elsewhere
    • Code first underlying disease, as:
      • myocarditis (acute):
        • influenzal (487.8)
        • tuberculous (017.9)
    • Excludes: myocarditis (acute) (due to):
      • aseptic, of newborn (074.23)
      • Coxsackie (virus) (074.23)
      • diphtheritic (032.82)
      • meningococcal infection (036.43)
      • syphilitic (093.82)
      • toxoplasmosis (130.3)
  • 422.9 Other and unspecified acute myocarditis
    • 422.90 Acute myocarditis, unspecified
      • Acute or subacute (interstitial) myocarditis
    • 422.91 Idiopathic myocarditis
      • Myocarditis (acute or subacute):
        • Fiedler's
        • giant cell
        • isolated (diffuse) (granulomatous)
        • nonspecific granulomatous
    • 422.92 Septic myocarditis
      • Myocarditis, acute or subacute:
        • pneumococcal
        • staphylococcal
      • Use additional code to identify infectious organism [e.g., Staphylococcus 041.1]
      • Excludes: myocarditis, acute or subacute:
        • in bacterial diseases classified elsewhere (422.0)
        • streptococcal (391.2)
    • 422.93 Toxic myocarditis
    • 422.99 Other
• 423 Other diseases of pericardium
  • Excludes: that specified as rheumatic (393)
  • 423.0 Hemopericardium
  • 423.1 Adhesive pericarditis
    • Adherent pericardium
    • Fibrosis of pericardium
    • Milk spots
    • Pericarditis:
      • adhesive
      • obliterative
    • Soldiers' patches
  • 423.2 Constrictive pericarditis
    • Concato's disease
    • Pick's disease of heart (and liver)
  • 423.8 Other specified diseases of pericardium
    • Calcification of pericardium
    • Fistula of pericardium
  • 423.9 Unspecified disease of pericardium
• 424 Other diseases of endocardium
  • Excludes: bacterial endocarditis (421.0-421.9)
    • rheumatic endocarditis (391.1, 394.0-397.9)
    • syphilitic endocarditis (093.20-093.24)
  • 424.0 Mitral valve disorders
    • Mitral (valve):
      • incompetence NOS of specified cause, except rheumatic
      • insufficiency NOS of specified cause, except rheumatic
      • regurgitation NOS of specified cause, except rheumatic
    • Excludes: mitral (valve):
      • disease (394.9)
      • failure (394.9)
      • stenosis (394.0)
      • the listed conditions:
        • specified as rheumatic (394.1)
        • unspecified as to cause but with mention of:
          • diseases of aortic valve (396.0-396.9)
          • mitral stenosis or obstruction (394.2)
  • 424.1 Aortic valve disorders
    • Aortic (valve):
      • incompetence NOS of specified cause, except rheumatic
      • insufficiency NOS of specified cause, except rheumatic
      • regurgitation NOS of specified cause, except rheumatic
      • stenosis NOS of specified cause, except rheumatic
    • Excludes: hypertrophic subaortic stenosis (425.1)
      • that specified as rheumatic (395.0-395.9)
      • that of unspecified cause but with mention of diseases of mitral valve (396.0-396.9)
  • 424.2 Tricuspid valve disorders, specified as nonrheumatic
    • Tricuspid valve:
      • incompetence of specified cause, except rheumatic
      • insufficiency of specified cause, except rheumatic
      • regurgitation of specified cause, except rheumatic
      • stenosis of specified cause, except rheumatic
    • Excludes: rheumatic or of unspecified cause (397.0)
  • 424.3 Pulmonary valve disorders
    • Pulmonic:
      • incompetence NOS
      • insufficiency NOS
      • regurgitation NOS
      • stenosis NOS
    • Excludes: that specified as rheumatic (397.1)
  • 424.9 Endocarditis, valve unspecified
    • 424.90 Endocarditis, valve unspecified, unspecified cause
      • Endocarditis (chronic):
        • NOS
        • nonbacterial thrombotic
      • Valvular:
        • incompetence of unspecified valve,unspecified cause
        • insufficiency of unspecified valve,unspecified cause
        • regurgitation of unspecified valve,unspecified cause
        • stenosis of unspecified valve,unspecified cause
      • Valvulitis (chronic)
    • 424.91 Endocarditis in diseases classified elsewhere
      • Code first underlying disease, as:
        • atypical verrucous endocarditis [Libman-Sacks] (710.0)
        • disseminated lupus erythematosus (710.0)
        • tuberculosis (017.9)
      • Excludes: syphilitic (093.20-093.24)
    • 424.99 Other
      • Any condition classifiable to 424.90 with specified cause, except rheumatic
      • Excludes: endocardial fibroelastosis (425.3)
        • that specified as rheumatic (397.9)
• 425 Cardiomyopathy
  • Includes: myocardiopathy
  • 425.0 Endomyocardial fibrosis
  • 425.1 Hypertrophic obstructive cardiomyopathy
    • Hypertrophic subaortic stenosis (idiopathic)
  • 425.2 Obscure cardiomyopathy of Africa
    • Becker's disease
    • Idiopathic mural endomyocardial disease
  • 425.3 Endocardial fibroelastosis
    • Elastomyofibrosis
  • 425.4 Other primary cardiomyopathies
    • Cardiomyopathy:
      • NOS
      • congestive
      • constrictive
      • familial
      • hypertrophic
      • idiopathic
      • nonobstructive
      • obstructive
      • restrictive
    • Cardiovascular collagenosis
  • 425.5 Alcoholic cardiomyopathy
  • 425.7 Nutritional and metabolic cardiomyopathy
    • Code first underlying disease, as:
      • amyloidosis (277.3)
      • beriberi (265.0)
      • cardiac glycogenosis (271.0)
      • mucopolysaccharidosis (277.5)
      • thyrotoxicosis (242.0-242.9)
    • Excludes: gouty tophi of heart (274.82)
  • 425.8 Cardiomyopathy in other diseases classified elsewhere
    • Code first underlying disease, as:
      • Friedreich's ataxia (334.0)
      • myotonia atrophica (359.2)
      • progressive muscular dystrophy (359.1)
      • sarcoidosis (135)
    • Excludes: cardiomyopathy in Chagas' disease (086.0)
  • 425.9 Secondary cardiomyopathy, unspecified
• 426 Conduction disorders
  • 426.0 Atrioventricular block, complete
    • Third degree atrioventricular block
  • 426.1 Atrioventricular block, other and unspecified
    • 426.10 Atrioventricular block, unspecified
      • Atrioventricular [AV] block (incomplete) (partial)
    • 426.11 First degree atrioventricular block
      • Incomplete atrioventricular block, first degree
      • Prolonged P-R interval NOS
    • 426.12 Mobitz (type) II atrioventricular block
      • Incomplete atrioventricular block:
        • Mobitz (type) II
        • second degree, Mobitz (type) II
    • 426.13 Other second degree atrioventricular block
      • Incomplete atrioventricular block:
        • Mobitz (type) I [Wenckebach's]
        • second degree:
          • NOS
          • Mobitz (type) I
        • with 2:1 atrioventricular response [block]
      • Wenckebach's phenomenon
  • 426.2 Left bundle branch hemiblock
    • Block:
      • left anterior fascicular
      • left posterior fascicular
  • 426.3 Other left bundle branch block
    • Left bundle branch block:
      • NOS
      • anterior fascicular with posterior fascicular
      • complete
      • main stem
  • 426.4 Right bundle branch block
  • 426.5 Bundle branch block, other and unspecified
    • 426.50 Bundle branch block, unspecified
    • 426.51 Right bundle branch block and left posterior fascicular block
    • 426.52 Right bundle branch block and left anterior fascicular block
    • 426.53 Other bilateral bundle branch block
      • Bifascicular block NOS
      • Bilateral bundle branch block NOS
      • Right bundle branch with left bundle branch block (incomplete) (main stem)
    • 426.54 Trifascicular block
  • 426.6 Other heart block
    • Intraventricular block:
      • NOS
      • diffuse
      • myofibrillar
    • Sinoatrial block
    • Sinoauricular block
  • 426.7 Anomalous atrioventricular excitation
    • Atrioventricular conduction:
      • accelerated
      • accessory
      • pre-excitation
    • Ventricular pre-excitation
    • Wolff-Parkinson-White syndrome
  • 426.8 Other specified conduction disorders
    • 426.81 Lown-Ganong-Levine syndrome
      • Syndrome of short P-R interval, normal QRS complexes, and supraventricular tachycardias
    • 426.89 Other
      • Dissociation:
        • atrioventricular [AV]
        • interference
        • isorhythmic
      • Nonparoxysmal AV nodal tachycardia
  • 426.9 Conduction disorder, unspecified
    • Heart block NOS
    • Stokes-Adams syndrome
• 427 Cardiac dysrhythmias
  • Excludes: that complicating:
    • abortion (634-638 with .7, 639.8)
    • ectopic or molar pregnancy (639.8)
    • labor or delivery (668.1, 669.4)
  • 427.0 Paroxysmal supraventricular tachycardia
    • Paroxysmal tachycardia:
      • atrial [PAT]
      • atrioventricular [AV]
      • junctional
      • nodal
  • 427.1 Paroxysmal ventricular tachycardia
    • Ventricular tachycardia (paroxysmal)
  • 427.2 Paroxysmal tachycardia, unspecified
    • Bouveret-Hoffmann syndrome
    • Paroxysmal tachycardia:
      • NOS
      • essential
  • 427.3 Atrial fibrillation and flutter
    • 427.31 Atrial fibrillation
    • 427.32 Atrial flutter
  • 427.4 Ventricular fibrillation and flutter
    • 427.41 Ventricular fibrillation
    • 427.42 Ventricular flutter
  • 427.5 Cardiac arrest
    • Cardiorespiratory arrest
  • 427.6 Premature beats
    • 427.60 Premature beats, unspecified
      • Ectopic beats
      • Extrasystoles
      • Extrasystolic arrhythmia
      • Premature contractions or systoles NOS
    • 427.61 Supraventricular premature beats
      • Atrial premature beats, contractions, or systoles
    • 427.69 Other
      • Ventricular premature beats, contractions, or systoles
  • 427.8 Other specified cardiac dysrhythmias
    • 427.81 Sinoatrial node dysfunction
      • Sinus bradycardia:
        • persistent
        • severe
      • Syndrome:
        • sick sinus
        • tachycardia-bradycardia
    • Excludes: sinus bradycardia NOS (427.89)
    • 427.89 Other
      • Rhythm disorder:
        • coronary sinus
        • ectopic
        • nodal
      • Wandering (atrial) pacemaker
      • Excludes: carotid sinus syncope (337.0)
        • reflex bradycardia (337.0)
        • tachycardia NOS (785.0)
  • 427.9 Cardiac dysrhythmia, unspecified
    • Arrhythmia (cardiac) NOS
• 428 Heart failure
  • Excludes: rheumatic (398.91)
    • that complicating:
      • abortion (634-638 with .7, 639.8)
      • ectopic or molar pregnancy (639.8)
      • labor or delivery (668.1, 669.4)
    • that due to hypertension (402.0-402.9 with fifth-digit 1)
  • 428.0 Congestive heart failure
    • Congestive heart disease
    • Right heart failure (secondary to left heart failure)
  • 428.1 Left heart failure
    • Acute edema of lung with heart disease NOS or heart failure
    • Acute pulmonary edema with heart disease NOS or heart failure
    • Cardiac asthma
    • Left ventricular failure
  • 428.9 Heart failure, unspecified
    • Cardiac failure NOS
    • Heart failure NOS
    • Myocardial failure NOS
    • Weak heart
• 429 Ill-defined descriptions and complications of heart disease
  • 429.0 Myocarditis, unspecified
    • Myocarditis (with mention of arteriosclerosis):
      • NOS (with mention of arteriosclerosis)
      • chronic (interstitial) (with mention of arteriosclerosis)
      • fibroid (with mention of arteriosclerosis)
      • senile (with mention of arteriosclerosis)
    • Use additional code to identify presence of arteriosclerosis
    • Excludes: acute or subacute (422.0-422.9)
      • rheumatic (398.0)
        • acute (391.2)
      • that due to hypertension (402.0-402.9)
  • 429.1 Myocardial degeneration
    • Degeneration of heart or myocardium (with mention of arteriosclerosis):
      • fatty (with mention of arteriosclerosis)
      • mural (with mention of arteriosclerosis)
      • muscular (with mention of arteriosclerosis)
    • Myocardial (with mention of arteriosclerosis):
      • degeneration (with mention of arteriosclerosis)
      • disease (with mention of arteriosclerosis)
    • Use additional code to identify presence of arteriosclerosis
    • Excludes: that due to hypertension (402.0-402.9)
  • 429.2 Cardiovascular disease, unspecified
    • Arteriosclerotic cardiovascular disease [ASCVD]
    • Cardiovascular arteriosclerosis
    • Cardiovascular:
      • degeneration (with mention of arteriosclerosis)
      • disease (with mention of arteriosclerosis)
      • sclerosis (with mention of arteriosclerosis)
    • Use additional code to identify presence of arteriosclerosis
    • Excludes: that due to hypertension (402.0-402.9)
  • 429.3 Cardiomegaly
    • Cardiac:
      • dilatation
      • hypertrophy
    • Ventricular dilatation
    • Excludes: that due to hypertension (402.0-402.9)
  • 429.4 Functional disturbances following cardiac surgery
    • Cardiac insufficiency following cardiac surgery or due to prosthesis
    • Heart failure following cardiac surgery or due to prosthesis
    • Postcardiotomy syndrome
    • Postvalvulotomy syndrome
    • Excludes: cardiac failure in the immediate postoperative period (997.1)
  • 429.5 Rupture of chordae tendineae
  • 429.6 Rupture of papillary muscle
  • 429.7 Certain sequelae of myocardial infarction, not elsewhere classified
    • Use additional code to identify the associated myocardial infarction:
      • with onset of 8 weeks or less (410.00-410.92)
      • with onset of more than 8 weeks (414.8)
    • Excludes: congenital defects of heart (745, 746)
      • coronary aneurysm (414.11)
      • disorders of papillary muscle (429.6, 429.81)
      • postmyocardial infarction syndrome (411.0)
      • rupture of chordae tendineae (429.5)
    • 429.71 Acquired cardiac septal defect
      • Excludes: acute septal infarction (410.00-410.92)
    • 429.79 Other
      • Mural thrombus (atrial) (ventricular) acquired, following myocardial infarction
  • 429.8 Other ill-defined heart diseases
    • 429.81 Other disorders of papillary muscle
      • Papillary muscle:
        • atrophy
        • degeneration
        • dysfunction
        • incompetence
        • incoordination
        • scarring
    • 429.82 Hyperkinetic heart disease
    • 429.89 Other
      • Carditis
      • Excludes: that due to hypertension (402.0-402.9)
  • 429.9 Heart disease, unspecified
    • Heart disease (organic) NOS
    • Morbus cordis NOS
    • Excludes: that due to hypertension (402.0-402.9)